胱抑素B/半胱氨酸蛋白酶抑制剂B抗体Anti-Cystatin BCPI B; CST6; CSTB; Cystatin B; CYTB; EPM1; Liver thiol proteinase inhibitor; PME; STFB; CH
360TIYO.COM-上海田源公司

性能参数：

中文名称：胱抑素B/半胱氨酸蛋白酶抑制剂B抗体
英文名称：Anti-Cystatin B
别名：CPI B; CST6; CSTB; Cystatin B; CYTB; EPM1; Liver thiol proteinase inhibitor; PME; STFB; CH
包装号：G320
产地：中国大陆/进口产品
商标/品牌：Santa、Abcam、MBL、BD、Cell Signaling Technology
供应商：田源试剂 TR、新试剂 NR
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产品详细描述

产品介绍：The Cystatin superfamily encompasses proteins that contain multiple Cystatin like sequences. Some of the members are active Cysteine protease inhibitors, while others have lost or perhaps never acquired this inhibitory activity. There are three inhibitory families in the superfamily, including the type 1 Cystatins （Stefins）, type 2 Cystatins ａnd Kininogens. Stefin B functions as an intracellular thiol protease inhibitor. The protein is able to form a dimer stabilized by noncovalent forces, inhibiting papain ａnd cathepsins l, h ａnd b. The protein is thought to play a role in protecting against the proteases leaking from lysosomes. Evidence indicates that mutated forms of this protein are responsible for the primary defects in patients with progressive myoclonic epilepsy.Subcellular Location : Cytoplasm. Nucleus.Involvement in disease: Defects in CSTB are the cause of progressive myoclonic epilepsy type 1 （EPM1） . EPM1 is an autosomal recessive disorder characterized by severe, stimulus-sensitive myoclonus ａnd tonic-clonic seizures. The onset, occurring between 6 ａnd 13 years of age, is characterized by convulsions. Myoclonus begins 1 to 5 years later. The twitchings occur predominantly in the proximal muscles of the extremities ａnd are bilaterally symmetrical, although asynchronous. At first small, they become late in the clinical course so violent that the victim is thrown to the floor. Mental deterioration ａnd eventually dementia develop.

胱抑素B/半胱氨酸蛋白酶抑制剂B抗体的质量标准：

■其它名称：	CPI B; CST6; CSTB; Cystatin B; CYTB; EPM1; Liver thiol proteinase inhibitor; PME; STFB; CH
■交叉反应：	hu, mo, rat, pig
■产品类型：	一抗
■应用领域:	/肿瘤/细胞生物/免疫学/转录调节因子
■蛋白分子：	predicted molecular weight: 14kDa
■浓度值：	1mg/1ml
■物理性状：	Lyophilized or Liquid
■免疫原：	KLH conjugated synthetic peptide derived from human Cystatin B
■亚型：	polyclonal
■纯化方法：	affinity purified by Protein A
■保存液：	0.01M PBS, pH 7.4 with 10 mg/ml BSA ａnd 0.1% Sodium azide
■应用技术：	//ELISA=1:500-1000//IP=1:20-100//IHC-P=1:100-500//IHC-F=1:100-500//IF=1:100-500（石蜡切片需做抗原修复）/not yet tested in other applications./optimal dilutions/concentrations should be determined by the end user.
■保存环境：	Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month ａnd for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.

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质量投诉流程
1、向我们的客户服务部反应投诉原因及订单信息。
2、向我们发送投诉相关的证明材料。
3、田源时间进行质量投诉调查及处理调查结果。
4、田源将联系客户并提供质量投诉处理结果。

友情提醒：
部分进口产品投诉须按照进口产品要求的检测方法提供证据。
由于化学产品的特殊性，恕不接受以下投诉：
1、超过质量投诉期的进口产品投诉
2、非质量报告提及的指标投诉

胱抑素B/半胱氨酸蛋白酶抑制剂B抗体Anti-Cystatin B的相关产品目录：







1mg/1ml 胱抑素B/半胱氨酸蛋白酶抑制剂B抗体 Anti-Cystatin B CPI B; CST6; CSTB; Cystatin B; CYTB; EPM1; Liver thiol proteinase inhibitor; PME; STFB; CH的来源为Rabbit，其相关产品：免疫组化常用试剂免疫印迹常用试剂各种标记二抗

查询其它抗体目录请点击本公司化工仪器网链接：http://www.chem17.com/st233816/erlist_675408.html

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