产品展示
FECH/Ferrochelatase铁螯合酶抗体
点击次数：240发布时间：2012/12/5 14:45:14
更新日期：2024/9/5 14:43:01
所 在 地：中国大陆
产品型号：BY-9521R
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详细内容
货号：BY-9521R
英文名称：Anti-FECH/Ferrochelatase
中文名称：铁螯合酶抗体
其他名称：名EPP;FCE;Ferrochelatase （protoporphyria）;Ferrochelatase;Ferrochelatase mitochondrial;Heme synthetase;Protoheme ferro lyase.
抗体来源：Rabbit
克隆类型：polyclonal
蛋白分子量：predicted molecular weight: 48kDa
纯化方法：affinity purified by Protein A
交叉反应：hu, rat, mo, chicken, cow, dog
产品介绍：Ferrochelatase catalyzes the insertion of the ferrous form of iron into protoporphyrin IX in the heme synthesis pathway, ａnd is localised in the mitochondrion. Defects in ferrochelatase are associated with protoporphyria. Two transcript variants encoding different isoforms have been found for this gene. Porphyrias are a group of inherited or acquired disorders of certain enzymes in the heme biosynthetic pathway （also called porphyrin pathway）. They are broadly classified as hepatic porphyrias or erythropoietic porphyrias, based on the site of the overproduction ａnd mainly accumulation of the porphyrins （or their chemical precursors）. They manifest with either skin problems, or neurological complications, or occasionally both.Subcellular Location : Mitochondrion inner membrane; Peripheral membrane protein; Matrix side.
