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Anti-ABATγ氨基丁酸转氨酶抗体
点击次数：269发布时间：2012/12/26 3:36:07
更新日期：2024/9/5 14:43:27
所 在 地：其它
产品型号：BY-4234R
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货号：BY-4234R
英文名称：Anti-ABAT
中文名称：γ氨基丁酸转氨酶抗体
其他名称：mitochondrial; （S） 3 amino 2 methylpropionate transaminase; （S）-3-amino-2-methylpropionate transaminase; 4 aminobutyrate aminotransferase; 4 aminobutyrate aminotransferase, mitochondrial; 4-aminobutyrate aminotransferase; ABAT; GABA aminotransferase; GABA AT; GABA T; GABA transaminase; GABA transferase; GABA-AT; GABA-T; GABAT; GABT_HUMAN; Gamma amino N butyrate transaminase; Gamma-amino-N-butyrate transaminase; L AIBAT; L-AIBAT; LAIBAT.
抗体来源：Rabbit
克隆类型：polyclonal
蛋白分子量：predicted molecular weight: 56kDa
纯化方法：affinity purified by Protein A
交叉反应：hu, mo, rat, hrs, cow, pig
产品介绍：Catalyzes the conversion of gamma-aminobutyrate ａnd L-beta-aminoisobutyrate to succinate semialdehyde ａnd methylmalonate semialdehyde, respectively. Can also convert delta-aminovalerate ａnd beta-alanine.Function : Catalyzes the conversion of gamma-aminobutyrate ａnd L-beta-aminoisobutyrate to succinate semialdehyde ａnd methylmalonate semialdehyde, respectively. Can also convert delta-aminovalerate ａnd beta-alanine.Subunit : Homodimer; disulfide-linked.Subcellular Location : Mitochondrion matrix.Tissue Specificity : Liver > pancreas > brain > kidney > heart > placenta.DISEASE : Defects in ABAT are a cause of gamma-aminobutyrate transaminase deficiency （GABA-AT deficiency） [MIM:613163]. The phenotype of this deficiency includes psychomotor retardation, hypotonia, hyperreflexia, lethargy, refractory seizures, ａnd EEG abnormalities.Similarity : Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family.
